Ichthyosis Hystrix : a case report Qazi
نویسندگان
چکیده
A six year old female child with generalized hyperpigmented hyperkeratotic verrucous plaques with nail and dental abnormalities suggestive of ichthyosis hystrix type of epidermal nevus is being reported in view of the rarity of this condition.
منابع مشابه
Curth-Macklin Ichthyosis Hystrix of Curth-Macklin
Ichthyosis hystrix of Curth-Macklin ( IHCM) is an extremely rare keratinization disorder, with verrucous to hystrixlike hyperkeratotic plaques of varying extent. The diagnosis is based on a distinctive pattern of epidermolytic hyperkeratosis and the presence of binucleate cells under light microscopy, as well as unique electron microscopic findings of continuous perinuclear tonofibril shells in...
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